Case Report of long-term follow-up of an unusual Oral Rhabdomyosarcoma with an intraosseous origin
Code: G-1042
Authors: Kamal Qaranizadeh, Mehrsa Zakershahrak, Afsoon Jalali Ara, Mehrnaz Zakershahrak © ℗
Schedule: Thursday 2023-12-07 10:45 on Unit Panel A
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Abstract:
Abstract
Purpose: Rhabdomyosarcoma is the most common soft tissue sarcoma in children and originates from skeletal muscle. Rhabdomyosarcoma is relatively uncommon in the oral cavity, and the involvement of the jaws is extremely rare (only 0.04 % of all head and neck malignancies). This paper aimed to report an exceptionally rare oral rhabdomyosarcoma with intraosseous origin (jawbone) in a 12-year-old boy with a novel combined treatment and assess the long-term efficacy of surgical treatment and its impact on the patient's health. Methods: After several inefficient chemotherapy sessions, the tumor was removed with Debulking surgery. Due to the patient's young age, the surgical plan was modified to prevent psychological and social problems, decrease post-op consequences such as disabilities, and preserve the patient's look. In this case, a marginal resection from both inside and outside the mouth was selected, resulting in a thorough resection of the tumor to preserve mandibular continuity. Results: After post-surgical chemotherapy, x-rays showed no abnormalities or metastasis. The patient was scheduled for annual follow-up appointments to ensure their long-term functionality and satisfaction with the treatment. Conclusion: So far, nearly a decade post-surgery, the patient is alive, healthy, functional, and shows no signs of tumor recurrence.
Keywords
Keywords: Debulking surgery; sarcoma; Muscle Neoplasms; Rhabdomyosarcoma
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